After the news that Chris Hemsworth is genetically predisposed to Alzheimer’s, thousands of Celine Dion fans have bad news: the singer has been diagnosed with Alzheimer’s strict person syndrome (SPS)a progressive neurological disorder and a rare disease that affects one or two of every million people each year.
Like all neurological diseases, SPS is certainly a very debilitating patient condition. those who suffer from severe muscle spasms and muscle stiffness in the trunk, arms, and legs. For Dion, the disease also affects his vocal cords, which causes him to be unable to sing.
The discomfort can also cause: increased sensitivity to sound, stress, and physical contact, triggers spasms and worsens to the point of making walking difficult or forcing the patient into a wheelchair. Currently, doctors do not know exactly what causes the disease, although there is a theory that it is an autoimmune reaction that attacks the body’s protein glutamic acid decarboxylase (GAD).
The protein in question helps produce gamma-aminobutyric acid (GABA), which regulates motor neurons in the brain; if there is less GABA, the neurons will overreactcauses spasms. The disease is often diagnosed in conjunction with another autoimmune disease such as type 1 diabetes (this drug is delayed in patients) and is more common in cancer patients.
Unfortunately there is no cure for SPShowever, the condition can be alleviated with medications, immunotherapies, and some types of physical therapy.
Source: Every Eye